Developmental Malformations
Sturge-Weber syndrome
Jun. 23, 2024
This is an image preview.
Start a Free Account
to view the full image.
-
Nearly 3,000 illustrations, including video clips of neurologic disorders.
-
Every article is reviewed by our esteemed Editorial Board for accuracy and currency.
-
Full spectrum of neurology in 1,200 comprehensive articles.
-
Listen to MedLink on the go with Audio versions of each article.
Myoclonic and myoclonic-atonic seizures in a 6-year-old boy (video-EEG)
Video EEG demonstrates myoclonic and myoclonic-atonic seizures in a 6-year-old boy with epilepsy with myoclonic-atonic seizures. The background activity is normal, but there are frequent (at least every 10 seconds) 3 to 6 Hz generalized spike/polyspike waves with anterior maximum. They are brief, lasting one to four seconds. These are frequently associated with single jerks, mainly of the shoulders, but also, on other occasions, of the thumb or eyelids. The jerks occur simultaneously with the first or the second polyspike-wave complex of the discharges. Some jerks are followed by atonic attacks. The EEG also showed brief (less than 0.5 s) abortive 1.5 Hz generalized spike/polyspike waves with anterior maximum and an alternating, but not consistent, side emphasis. There were no clinical manifestations. The paroxysmal discharges occurred with eyes opened and closed, spontaneously, and during overbreathing. Intermittent photic stimulation did not evoke photoparoxysmal responses. (Contributed by C P Panayiotopoulos.)